Congenital absence of one pulmonary artery, while not a common anomaly, is nonetheless not rare. Over 100 cases of various modifications of this abnormality have been reported, and we have recently prepared a detailed analysis of 78 of these cases1 in which an adequate amount of information was available for detailed study. Since an excessive pulmonary blood flow, because of associated shunts, is common, and since blood from the pulmonary artery in this anomaly all flows through one lung only, the development of pulmonary hypertension is a frequent occurrence and may result in the death of the patient in early childhood. For this reason it is impressive to recognize the lesion so that curative surgery may be undertaken early.
This report concerns what appears to be an almost unique modification of unilateral absent pulmonary artery in which absence of the left pulmonary artery is associated with a right aortic