TY  - JOUR
T1  - SUrgical management of the succinate dehydrogenase–associated familial paraganglioma syndromes
AU  - Cocieru A, Saldinger PF
Y1  - 2012/01/01
N1  - 10.1001/archsurg.2011.552
JO  - Archives of Surgery
SP  - 89
EP  - 91
VL  - 147
IS  - 1
N2  - Paragangliomas are rare neuroendocrine tumors arising from the neural crest cells in the extra-adrenal location. Paragangliomas can be sporadic or associated with a range of endocrine and genetic syndromes in 25% to 30% of all cases. Specifically, succinate dehydrogenase gene mutations are involved in the development of paraganglioma syndromes type 1 through type 4. In this article, we will describe 2 cases of succinate dehydrogenase–associated familial paraganglioma syndrome and provide a review of the existing literature on the condition's etiologic factors, diagnosis, and management.
SN  - 0004-0010
M3  - doi: 10.1001/archsurg.2011.552
UR  - http://dx.doi.org/10.1001/archsurg.2011.552
ER  -